Main description:

Interest in interstitial lung diseases (ILDs) has risen in recent years. A large volume of basic and clinical research has increased our understanding of the pathogenesis of idiopathic pulmonary fibrosis (IPF) and non-IPF fibrotic ILDs. The ILD field is now evolving rapidly, with major implications for practical management. This Monograph provides expert clinical guidance on these difficult diseases, which will be helpful to both respiratory and nonrespiratory physicians alike. The initial chapters consider diagnostic issues, pulmonary function tests and techniques that are currently in development. The book then goes on to cover a variety of pulmonary manifestations of very different disease entities, such as connective tissue diseases, systemic vasculitis and much more.

Contents:

Multidisciplinary approach to systemic disease: benefits for diagnosis and management of complex disorders; Pulmonary function tests in multisystem disorders: prejudices and pitfalls; Quantitative CT analysis in ILD and the use of artificial intelligence on imaging of ILD; Pulmonary involvement in rheumatoid arthritis; Pulmonary involvement in inflammatory myopthies; Pulmonary involvement in systemic sclerosis; Pulmonary involvement in systemic lupus erythematosus, Sjoegren syndrome and mixed connective tissue disease; Pulmonary involvement in antiphospholipid syndrome; Interstitial pneumonia with autoimmune features; Microscopic polyangiitis and granulomatosis with polyangiitis; Diffuse alveolar haemorrhage; Eosinophilic granulomatosis with polyangiitis; Pulmonary involvement in Takayasu arteritis and Behcet disease; Airway and lung involvement in inflammatory bowel disease; the lung in liver disease: hepatopulmonary syndrome and portopulmonary hypertension; Lung complications of neuromuscular diseases; Amyloidosis and the lung; Trafficking and lysosomal storage disorders; Pulmonary involvement in haematological disorders and bone marrow transplant recipients; Pulmonary involvement of systemic histiocytic disorders; Pulmonary involvement in immunodeficiency; Telomere syndrome and the lung; Sarcoidosis: pulmonary manifestations and management